Primitive Neuroectodermal tumor / Ewing’s sarcoma of the prostate in a young Indian adult – an extremely rare case report

Abstract

We present an extremely rare case of Primitive Neuroectodermal tumor (PNET) / Ewing’s sarcoma of the prostate in a 40 years old Indian male who presented with pedal edema and dysuria. Ultrasonography was performed which showed a pelvic mass between urinary bladder and rectum. Fine Needle Aspiration Cytology diagnosis of a Malignant round cell tumor- PNET / Ewing’s sarcoma was made, which was confirmed by Biopsy and Immunohistochemistry (IHC). The prognosis of PNET / Ewing’s sarcoma of prostate is very poor since it is one of the most aggressive tumors and rare disease entity. To the best of our knowledge, this is the 10 th case documented internationally and only second from Indian subcontinent.